Suggested remit: To appraise the clinical and cost effectiveness of intrathecal onasemnogene abeparvovec within its marketing authorisation for treating spinal muscular atrophy.

Status:
In progress
Technology type:
Medicine
Decision:
Selected
Reason for decision:
Anticipate the topic will be of importance to patients, carers, professionals, commissioners and the health of the public to ensure clinical benefit is realised, inequalities in use addressed, and help them make the best use of NHS resources
Process:
STA Standard
ID number:
6556

Provisional Schedule

Committee meeting: 1:
07 July 2026
Expected publication:
26 August 2026
Expected publication:
28 October 2026

Project Team

Project lead
Leena Issa

Email enquiries

If you have any queries please email TACommC@nice.org.uk


External Assessment Group:
BMJ Technology Assessment Group (BMJ-TAG), BMJ

Stakeholders

Companies sponsors
Novartis Pharmaceuticals UK (onasemnogene abeparvovec)
Others
Department of Health and Social Care
 
NHS England
Patient carer groups
ACE SMA
 
Ally Cadence Trust for Spinal Muscular Atrophy
 
Arthritis and Musculoskeletal Alliance
 
Brain and Spine Foundation
 
Brain Charity
 
Gene People
 
Genetic Alliance UK
 
Jnetics
 
Muscular Dystrophy UK
 
Neurological Alliance
 
Pathfinders Neuromuscular Alliance
 
Rally Round Rupert
 
South Asian Health Foundation
 
Specialised Healthcare Alliance
 
Spinal Muscular Atrophy UK
 
The Annabelle Rose Foundation for Spinal Muscular Atrophy
 
TREAT-SMA
Professional groups
Adult SMA Reach
 
Association of Anaesthetists
 
Association of British Neurologists
 
Association of Chartered Physiotherapists in Neurology
 
Association of Genetic Nurses and
 
Counsellors
 
Association of Paediatric Chartered Physiotherapists
 
Association of Surgeons of Great Britain and Ireland
 
British Dietetic Association
 
British Geriatrics Society
 
British Myology Society
 
British Neuropathological Society
 
British Orthopaedic Association
 
British Paediatric Neurology Association
 
British Society for Children's Orthopaedic Surgery
 
British Society for Gene and Cell Therapy
 
British Society for Genetic Medicine
 
British Society for Rheumatology
 
British Society of Physical and Rehabilitation Medicine
 
Chartered Society of Physiotherapy
 
Institute of Neurology
 
Institute of Neurology and Neurosurgery
 
National Neuroscience Advisory Group
 
Neonatal and Paediatric Pharmacists Group
 
Primary Care and Community Neurology Society
 
Royal College of Anaesthetists
 
Royal College of General Practitioners
 
Royal College of Nursing
 
Royal College of Paediatrics and Child Health
 
Royal College of Pathologists
 
Royal College of Physicians
 
Royal College of Surgeons
 
Royal Pharmaceutical Society
 
Royal Society of Medicine
 
SMA Reach UK
 
Society for Endocrinology
 
Treat-NMD
 
UK Clinical Pharmacy Association
Associated public health groups
Public Health Wales
 
UK Health Security Agency
Comparator companies
Biogen (nusinersen)
 
Novartis Pharmaceuticals UK (onasemnogene abeparvovec) [intravenous infusion]
 
Roche (risdiplam)
General commentators
All Wales Therapeutics and Toxicology Centre
 
Allied Health Professionals Federation
 
Board of Community Health Councils in Wales
 
British National Formulary
 
Care Quality Commission
 
Department of Health - Northern Ireland
 
Healthcare Improvement Scotland
 
Medicines and Healthcare products Regulatory Agency
 
National Association of Primary Care
 
National Pharmacy Association
 
Neurological Alliance of Scotland
 
NHS Confederation
 
NHS Wales Joint Commissioning Committee
 
Scottish Medicines Consortium
 
Wales Neurological Alliance
 
Welsh Government
Relevant research groups
Bone Research Society
 
Brain Research UK
 
Chronic Pain Policy Coalition
 
Cochrane Musculoskeletal Group
 
Genomics England
 
John Walton Muscular Dystrophy Research Centre
 
MRC Centre for Neuromuscular Diseases
 
MRC Clinical Trials Unit
 
National Hospital for Neurology and Neurosurgery
 
National Institute for Health Research
 
Orthopaedic Research UK

Timeline

Key events during the development of the guidance:

Date Update
24 November 2025 Invitation to participate
02 October 2025 To appraise the clinical and cost effectiveness of OAV101 IT within its marketing authorisation for treating spinal muscular atrophy ID6556
04 August 2025 - 02 September 2025 Consultation on suggested remit, draft scope and provisional stakeholder list of consultees and commentators: 6556
04 August 2025 In progress. Scoping commencing
08 April 2025 Awaiting development. Status change linked to Topic Selection Decision being set to Selected

For further information on our processes and methods, please see our CHTE processes and methods manual